Double inlet left ventricle

In medicine, we denote by Single Ventricle or single-chamber heart a circle form of congenital heart malformations, which has formed during fetal development, only a functioning heart chamber ( ventricle). It includes very diverse forms, which have different effects on the circulatory system and the therapeutic approach. Common to all forms that really there is only one ventricle or a main chamber that her blood from both atria gets a " secondary chamber ", which receives its blood from the main chamber. Another criterion are the additions of the heart valves and thus the input and outflow of the chamber.

Molding

We distinguish between two basic forms, depending on whether the right ventricle ( pulmonary circulation ) or the left ventricle has ( systemic circulation ) are not sufficiently trained. These are then referred to by the ventricle as Single Ventricle with good working left ventricle and right ventricle working order.

After this initial allocation then the actual etiologies are also named as diagnoses:

  • Single Ventricle and in working with the left ventricle ( the right ventricle is not adequately trained ) Double inlet left ventricle ( = Dilv ) - Both AV valves or a common AV valve opening into the left ventricle.
  • Double outlet left ventricle ( = DOLV ) - aorta and pulmonary artery completely or to leave more than 50% of the functionally effective left ventricle
  • Pulmonary atresia
  • Tricuspid atresia
  • Single Ventricle and in working with the right ventricle ( the left ventricle is not adequately trained ) Double inlet right ventricle ( = DIRV ) - Both AV valves or a common AV valve opening into the right ventricle.
  • Double outlet right ventricle ( DORV = ) - incorrect disposal of the aorta from the right ventricle
  • Hypoplastic left heart syndrome ( HLHS = )

Therapy

Surgical treatment in the form of palliative surgery and an operation that improves the situation depends on the precise anatomical constellation and will be decided individually for each child.

  • Fontan operation in abnormalities of the right ventricle, especially closure of tricuspid and / or pulmonary
  • Norwood procedure with malformations of the left ventricle, especially in Hypoplastic Left Heart Syndrome
  • Heart transplantation as a possibility if both of the above operations are not promising and the child's condition requires it.
Medical guideline
256532
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