Koenen's tumor
Bourneville ( Pringle ) syndrome Epiloia
A Koenen's tumor (pronounced Ku: NEN - tumor), also known as periunguales fibroma ( periungual =, around the nail ') or subungual fibroma ( Subungual =, under the nail ' ), is a benign mesenchymal tumor ( a fibroma ), which the foot or toe nails produced in the region.
Description
Koenen tumors are a symptom of tuberous sclerosis ( also called Pringle 's disease ), an autosomal dominant hereditary disease. The benign tumors are skin-colored nodes that form in the foot or toe nails or beneath the nails and are typically 3-7 mm in size.
Therapy
Koenen tumors may optionally be removed surgically by excision or by CO2 laser.
Naming
The Koenen's tumor is named after the Dutch neurologist Joannes Henricus Maria Koenen, the 1932 photographic abbildete him for the first time in an article. The first description was in 1903 by the Munich physician Richard Kothe.
Further Reading
- A. DaCunha: Images in clinical medicine. Periungual fibromas. In: The New England Journal of Medicine. Volume 359, Number 13, September 2008, pp. 1381, ISSN 1533-4406. doi: 10.1056/NEJMicm073405. PMID 18,815,399th
- P. E. Ward, D. J. McCarthy: periungual fibroma. In: cutis; cutaneous medicine for the practitioner. Volume 46, Number 2, August 1990, pp. 118-124, ISSN 0011-4162. PMID 2,209,075th
- T. Kojima, T. Nagano, M. Uchida: periungual fibroma. In: The Journal of hand surgery. Volume 12, Number 3, May 1987 pp. 465-470, ISSN 0363-5023. PMID 3,584,898th