Congenital cystic adenomatoid malformation
The Cystic adenomatoid malformation of the lung ( CCAM abbreviation of engl: congenital cystic adenomatoid malformation ) is a congenital malformation, which belongs to the group of hamartomas.
Molding
Types according to Stocker:
- Type I: (50%) One or more cysts 2-10 cm in diameter, partly additionally smaller cysts. Some of the cysts contain mucus.
- Type II: (40 %) multiple small cysts of uniform 0.5-2 cm in diameter.
- Type III: (<10 %) microscopic cysts. In the imaging shows a solid mass.
Symptoms
Infections of the bronchi and the lungs, shortness of breath, respiratory failure, heart failure and failure to thrive.
Diagnostics
The CCAM can already be seen in the prenatal ultrasound. Close monitoring after diagnosis is necessary because it can lead to a rapid growth. However regress 56% of the discovered CCAMs.
After the birth: X-ray of the lungs, CT, possibly bronchoscopy, NMR
Therapy
If the child's death is feared by a strong increase in size before birth, prenatal open distance of the process can be carried out in an appropriate center.
If the CCAM makes symptoms, surgical removal is recommended that asymptomatic cases remains controversial.