Hereditary motor and sensory neuropathy

Hereditary motor and sensory neuropathy, HMSN abbreviated, are a group of inherited and chronic progressing nerve diseases ( neuropathy ) that capture only the peripheral nerves and their predominantly motor component. A common feature is the distal ( far hull ) beginning, gradually expanding central weakness with accompanying muscle wasting (atrophy ). The old designations with proper names are left increasingly in favor of the following Classification ( according to Dyck ).

  • HMSN I - Charcot -Marie -Tooth disease
  • HMSN II - Neural peroneal muscular atrophy
  • HMSN III - Dejerine -Sottas disease
  • HMSN IV - Refsum's syndrome
  • HMSN V - ( Hereditary spastic paraplegia )
  • HMSN VI - ( HMSN with optic atrophy )
  • HMSN VII - ( HMSN with retinitis pigmentosa)
Dejerine–Sottas disease
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