Sprengel's deformity

The Sprengelsche deformity or Sprengel deformity is a dysostosis with axial involvement, which manifests itself as a one shoulder wedding to stand with small scapula. Named after the German surgeon Otto Gerhard Karl Sprengel (1852-1915) named deformity may occur as part of the Klippel -Feil syndrome, but also together with other changes, such as scoliosis, rib malformations or spina bifida.

The cause inhibition of wandering down the shoulder blade system of level of the 5th HWK is caudally before the date of injury is assumed in the third month of pregnancy, familial aggregation is described.

Frequently found next to a shortening of the neck muscles a connective tissue or cartilaginous strand between the upper border of the scapula and vertebral appendages of the lower cervical spine. Is this bony pronounced, it is used as Omovertebralknochen, Os omo -vertebral referred, and can be seen on radiographs. In the other cases, this string in MRI (MRT) are presented.

Preferably girls are affected, the left side a bit more often, although the disease also can occur on both sides. Clinically, fixed the shoulder blade high level with Disabilities in the foreground and the accompanying kyphoscoliosis.