Trigonocephaly

The term trigonocephaly (Greek TRIGONOS τρίγωνος, triangular ', kephale κεφαλή, head ' ) is described in human medicine a special head shape, which is characterized by a triangular skull shape (triangle skull) and in particular really stand out a prominent, keel -like forehead.

In people with a Trigonocephalus there has been in development at an unusually early merger of the frontal suture ( metophische seam). As a result of this Verknöcherungsstörung the skull has received a triangular -acting form, in which the protruding forehead and tubers frontalia ( ossification of the frontal bone ) are missing, leading up to the development of a oxycephalus (pointed skull) may result.

Trigonocephaly is partly present as a symptom of a common chromosomal syndrome -related complex. They often than the average occurs in people with Partial Trisomy 3p, the Patau syndrome ( trisomy 13), Edwards syndrome ( trisomy 18), the Bohring -Opitz syndrome (C- syndrome / Opitz C trigonocephaly / Opitz trigonocephaly syndrome).

Due to the unusual head shape, the brain is forced to adapt accordingly. Whether and to what extent it leads to a reduction of the expected cognitive capabilities of the human and whether surgical intervention is necessary, is very different. The biggest dependency is here revealed in the type and severity of other symptoms. This also explains why is to be expected by surgical correction of head shape with only a cosmetic effect.