Angiodysplasia

As angiodysplasia ( Greek: ἀγγεῖον ( angeion ) vessel, δυσ ( dys ) ' miss- un- ', πλάσσειν ( plassein ) of πλάσσω form, shape ) refers to vascular malformations of arteries, veins or lymph vessels, which in enormous complexity and diversity may occur. Synonymous they are also referred to as vascular dysplasia.

• 2.3.1 Osler

Hamburger classification

Previously you could only describe these diseases and their pathological anatomy could not be detected. Depending on the vascular malformation syndrome received numerous names, partly for the same malformation. The assignment of a disease picture to one of these syndromes is not always possible and overlaps are possible. In 1988, The Hamburg classification avoids the syndrome concepts and tries to describe the angiodysplasia according to their anatomical and functional changes. On the one hand according to two forms trunkulär extratrunkulär and in which the disturbances in the embryonic development stages are taken into account.

Syndromes

Developmental Venous Anomaly

Developmental Venous Anomaly In (DVA ) is a benign, venous malformation in the brain. The anomaly consists of a bundle extended, medullary veins that converge on a strong central Drainagevene caliber.

Nevus flammeus

The port-wine stain or naevus flammeus is a benign lesion. The birthmark is based on a congenital malformation. Tiny blood vessels that run underneath the epidermis are expanded and pathologically prone to growths. The port wine stain may be evidence of other disease in some cases. Up to 30 syndromes have now been associated with the occurrence of a fire Malles to:

Sturge -Weber syndrome

The Sturge -Weber Syndrome is a congenital progressive disorder of the group of neurocutaneous phakomatoses. It is characterized by hohlräumige benign vascular tumors ( angiomas ) in the facial area, in the meninges, in the ipsilateral pia mater ( leptomeninges ) and the choroid of the eye ( choroid ). Affected children can have epileptic seizures, suffer glaucoma and mental retardation.

Klippel Trenaunay - Weber syndrome

Klippel Trenaunay - Weber syndrome is a malformation syndrome of the vessels, the. By a large port-wine stain, lymphangiomas, which is accompanied by partial gigantism of the trunk or extremities In addition, causal malformations of the deep blood and lymphatic system may occur.

Maffucci syndrome

The syndrome is characterized by a Enchondromatosis (multiple benign cartilage tumors) as well as deep cavernous hemangiomas and lymphangiomas of the skin and internal organs.

Hemangioma

A hemangioma ( strawberry mark ), is an embryonal tumor with endothelial proliferation and secondary education of the vessel lumen. A distinction Capillary Hemangioma, Cavernous Hemangioma, grape or berry -shaped hemangioma, hemangioma Sclerosing, planotuberosum hemangioma, hemangioma of the orbit and the hemangioma of the liver.

Kasabach -Merritt syndrome

When Kasabach -Merritt syndrome is the formation of benign, cavernous and large to giant hemangiomas. It is rather the benign Tufted angioma (synonym: Angioblastoma of Nakagawa ) before and during malignant epithelioid hemangioendothelioma Kaposi -like.

Pyogenic granuloma

The pyogenic granuloma is a benign vascular skin tumor from the group of hemangiomas. It is an exophytic vascular proliferation.

Vascular malformation

A vascular malformation ( vascular malformation ) is a malformation of one or more blood or lymph vessels. The vascular malformations include arteriovenous malformations ( AV malformations ), the cavernomas ( venous malformations ), and lymphatic malformations. A special form of a Lymphangiomes is the hygroma colli. Also the Gorham - Stout syndrome is associated with lymphangiomas gebracht.Meistens malformations are congenital, but show in the course of living a Größenprogredienz. The capillary malformations heard in the digestive tract of Osler's disease.

Osler

Osler's disease is an autosomal dominantly inherited disorder in which there is an abnormal dilation of blood vessels. These so-called telangiectasias can occur anywhere, can be found, however, particularly in the nose ( symptom nosebleeds ), mouth, face and the mucous membranes of the gastrointestinal tract, but they can also in the lungs, in the liver and in the brain occur, whereby - especially from the age of 40 - internal bleeding can occur, which may even have life-threatening consequences.

Heyde 's syndrome

The Heyde 's syndrome consists of a combination of acquired aortic stenosis and bleeding from malformed blood vessels of the ascending part of the colon. The anemia occurring through the bleeding is also regarded as part of the syndrome.

Kommerell diverticulum

When Kommerell diverticulum thereby ( descending aorta ) is a sac-like extension or protrusion of the aortic arch or the descending aorta in the case of an outgoing from the aorta, right subclavian artery ( subclavian artery ).

Crohn Hippel -Lindau

The disease Hippel -Lindau is a rare, hereditary tumor disease from the mold circle of so-called phakomatoses. The patients develop benign, tumor- like tissue changes ( Angioma ) primarily in the area of the retina of the eye and the cerebellum. In the central nervous system may also home to the brainstem and the spinal cord, the cerebrum rarely be affected. It is characteristic that develop tumors that consist of glomeruli. Many patients also have tissue changes in the area of the kidney ( renal cell carcinoma), adrenal gland ( pheochromocytoma ), and pancreas. In men, the epididymis may be affected.