Foix–Chavany–Marie syndrome

The Foix - Chavany -Marie syndrome, also under the synonyms of bilateral anterior operculum syndrome ( AOS) and faciopharyngoglossomasticatorischer diplegia known, a rare syndrome, bilateral lesions of the cerebral cortex in the central region is underlie and that and a dissociation of voluntary motor automatic ( emotional ) Motor leads in the face, chewing, and swallowing muscles. The patients are not able to perform voluntary movements in the mentioned muscles, for example, while involuntary emotional and reflex movements of the same muscles are intact.

The syndrome is named after the Erstbeschreibern Charles Foix, Jean Alfred Émile Chavany and Julien Marie.

Mark

Diagnostically relevant is the evidence of the cerebral cortex damage, consisting in a two-sided ( bilateral ) lesion opercula frontoparietalia. People with Foix - Chavany -Marie syndrome can not move willingly face, jaw, tongue and pharyngeal muscles. This means that it is not possible for them to move at will the facial muscles ( muscles of facial expression ) (eg, smile ), while involuntary muscle movements, as they take place about to cough or yawn, remain possible. Emotional facial expressions (eg when crying ) is retained, as the eyes are closed in sleep.

Diagnosis

The diagnosis is possible by magnetic resonance imaging. There is a bilateral lesion of the opercula frontoparietalia.