Moyamoya disease

As Moyamoya disease ( by Japanese moya moya "fog" ) refers to a disease of the brain vessels, in which there is a narrowing or blockage of brain arteries, usually the internal carotid artery and the middle cerebral artery, and at the thereby a relative anemia ( stroke and transient ischemic attack ) set in the brain. They form many small compensatory vessels from as collateral circulation. The name of the disease derives from the fact that many thin vessels with imaging modalities ( angiography ) look like a fog formations. The disease is rare in Europe, and occurs mainly in Asia (especially Japan ), the incidence of the disease, a bimodal peak - aged 2 to 10 years old and 30 to 40 years - shows. While the term " moyamoya disease " refers to the idiopathic form, the term " moyamoya syndrome " is used for the angiographic image in the context of other diseases such as atherosclerosis, Down syndrome, etc. irradiation sequence.

Patients with moyamoya disease tend to the development of cerebral infarction and cerebral hemorrhage. The clinical picture corresponds to these diseases. The diagnosis is made by angiography and magnetic resonance imaging and should be reserved for specialized centers.

In addition to a conservative treatment especially neurosurgical treatment bypass (bypass) appears promising. Here an operative connection between the temporal artery (arteria temporalis superficialis ) and a cerebral artery ( middle cerebral artery ) is placed.